Rhabdomyosarcoma is a soft-tissue tumor that arises from malignant mesenchymal cells.
Epidemiology
Rhabdomyosarcomas are the most common malignant intraorbital tumors in children[^1].
Classification
According to the WHO classification, rhabdomyosarcomas are divided into the following four distinct subtypes[^2]:
Embryonal rhabdomyosarcoma (ARMS)
Pleomorphic rhabdomyosarcoma (PRMS)
Spindle cell/sclerosing rhabdomyosarcoma (SRMS)
Alveolar rhabdomyosarcoma (ARMS)