Rhabdomyosarcoma

Last edit by Alaric Steinmetz on

Rhabdomyosarcoma is a soft-tissue tumor that arises from malignant mesenchymal cells.

Epidemiology

Rhabdomyosarcomas are the most common malignant intraorbital tumors in children[^1].

Classification

According to the WHO classification, rhabdomyosarcomas are divided into the following four different subtypes[^2]:

  • Embryonal rhabdomyosarcoma (ARMS)

  • Pleomorphic rhabdomyosarcoma (PRMS)

  • Spindle cell\/sclerosing rhabdomyosarcoma (SRMS)

  • Alveolar rhabdomyosarcoma (ARMS)

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