Papillary tumor of the pineal region (WHO Grade 2–3)

Last edited and medically reviewed by Alaric Steinmetz on 01.03.2025

Synonyms: PTPR, Papillary tumor of the pineal region

Papillary tumor of the pineal region is a rare neuroepithelial tumor that, depending on its histopathology, can be classified as WHO Grade 2 or 3 according to the 2021 CNS WHO classification[^1].

Historical background

This tumor entity was first described in 2003[^2].

Epidemiology

Papillary tumors of the pineal region account for approximately 1 % of all intracranial tumors[^1].

Imaging

Papillary tumor of the pineal region MRI — Sagittal MRI (T1 postcontrast sequence) of a histopathologically verified papillary tumor of the pineal region.

Papillary tumor of the pineal region — MRI images of three sagittal sequences (CISS, T1, and T1 with contrast enhancement) of a histopathologically verified papillary tumor of the pineal region.

Intraoperative

Endoscopic papillary tumor of the pineal region — Endoscopic intraoperative visualization of the tumor surface of a histopathologically verified papillary tumor of the pineal region.

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