McCune-Albright syndrome

Last edit by Alaric Steinmetz on

Synonyms: MAS

ICD-11: FB80.0

McCune-Albright syndrome is a very rare condition counted among the neurocutaneous syndromes, characterized by café-au-lait spots, endocrinological abnormalities, and disturbances in bone metabolism.

Clinical Features

McCune-Albright syndrome is characterized by the following manifestations[^1] [^2]:

  • Fibrous dysplasia (typically polyostotic)

  • Café-au-lait spots

  • Pseudoprecocious puberty