Hydranencephaly

Last edit by Alaric Steinmetz on

Synonyms: Hydranencephaly

ICD-10: Q04.3

Hydranencephaly is a rare brain malformation where the brain hemispheres are largely absent.

Pathology

Instead of functional nerve tissue, large fluid-filled cavities are found. In hydranencephaly, the meninges and the skull bone are intact and this condition is associated with a normal head shape[^1].

Variations

If only one half of the brain is affected, it is referred to as hemihydranencephaly.